This website uses cookies. By continuing you are agreeing to our privacy policy.

Souheil El-Chemaly, MD, MPH

Research Awards Nationwide Recipient (2014-2016)

Brigham and Women's Hospital, Boston, MA
Identifying the Mechanisms Underlying Hermansky-Pudlak Syndrome

Hermansky-Pudlak syndrome (HPS) is a rare inherited disease which causes scarring of the lungs with limited treatment options. We will explore how HPS fibroblasts differ from those in normal lungs and whether treatment can make them behave like normal fibroblasts. These studies will be performed in zebrafish embryos, a new model for studying HPS pulmonary fibrosis which may have use in identifying new treatment targets. Understanding the underlying mechanisms of HPS may accelerate the discovery of therapies for more common lung diseases like cystic fibrosis and idiopathic pulmonary fibrosis.

Sign up for the latest lung health news delivered right to your inbox.

Join more than 500,000 people who receive research updates, inspiring stories, health information and more.

Please leave this field empty

Thanks for joining us in the fight for healthy lungsWe look forward to keeping you informed about vaping and e-cigarettes, and sharing the latest lung health news with you.
Blank Section Header
Red button with telephone
Ask An Expert

Questions about your lung health? Need help finding healthcare? Call 1-800-LUNGUSA.

Get help
Red button of two hand prints
We need your generous support

Make a difference by delivering research, education and advocacy to those impacted by lung disease.

Button of turquoise LUNG FORCE swirl
What is LUNG FORCE?

LUNG FORCE unites women and their loved ones across the country to stand together in the fight against lung cancer.

Get involved
Join the fight for healthy lungs and healthy air.
Donate Now.