Primary Pulmonary Hypertension

Primary pulmonary hypertension (PPH) is a rare lung disease that leads to narrowing of the blood vessels of the lungs. This narrowing worsens over time and causes high blood pressure in these blood vessels. It is sometimes call unexplained pulmonary hypertension because it describes pulmonary hypertension when there is no underlying heart or lung disease causing the high blood pressure. Symptoms of PPH can develop so slowly that you may have PPH for years without knowing it. Treatments for PPH focus on symptoms and include several medications, surgery, as well as lifestyle changes.

PPH is one type of pulmonary hypertension. The American Lung Association also provides patients with information about pulmonary arterial hypertension (PAH).